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What is Usher Syndrome?

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Usher Syndrome is a genetic condition characterized by deafness at birth or progressive hearing loss and progressive vision loss.

Symptoms of Usher Syndrome type 1

  • Bilateral profound deafness from birth
  • Vestibular (balance) problems from birth that can include
    • Poor head control as an infant
    • Arching of back as an infant
    • Late sitting
    • Late walking at age 18 months or later and then with poor balance for the first few years
    • Decreasing night vision beginning in childhood to adolescence
  • For more information on Usher Syndrome, visit the NIDCD website.

Currently, there is no cure for Usher Syndrome. While cochlear implants have greatly ameliorated the most major impacts of deafness for those who receive them as babies, there is no cure for blindness. Early identification and educational programs provide support to those affected, but in a world teeming with major technological advances in medicine, this simply isn't good enough. Targeted research is needed to enable a cure.

What is Usher 1F? - in ASL